Journal of the Formosan Medical Association
Volume 106, Issue 6 , Pages 485-489, 2007

Jejunal and Multiple Mesenteric Calcifying Fibrous Pseudotumor Induced Jejunojejunal Intussusception

  • Hung-Hua Liang

      Affiliations

    • Department of Surgery, Taipei Medical University Hospital, Taipei, Taiwan
  • ,
  • Chiah-Yang Chai

      Affiliations

    • Department of Surgery, Taipei Medical University Hospital, Taipei, Taiwan
  • ,
  • Yun-Ho Lin

      Affiliations

    • Department of Pathology, Taipei Medical University Hospital, Taipei, Taiwan
  • ,
  • Chii-Hong Lee

      Affiliations

    • Department of Pathology, Taipei Medical University Hospital, Taipei, Taiwan
  • ,
  • Chih-Hsiung Wu

      Affiliations

    • Department of Surgery, Taipei Medical University Hospital, Taipei, Taiwan
  • ,
  • Chun-Chao Chang

      Affiliations

    • Division of Gastroenterology, Department of Internal Medicine, Taipei Medical University Hospital, Taipei, Taiwan
    • Corresponding Author InformationCorrespondence to: Dr Chun-Chao Chang, Department of Internal Medicine, Taipei Medical University Hospital, 250 Wu-Hsing Street, Taipei 100, Taiwan

Received 20 July 2006; received in revised form 28 July 2006; accepted 7 November 2006.

Article Outline

We describe here a patient with an unusual presentation-mesenteric calcifying fibrous pseudotumor in association with jejunojejunal intussusception. This 25-year-old woman came to our emergency department with severe abdominal distension and intermittent epigastric cramping pain. She was found to have rebound tenderness and an ill-defined mass palpable in her lower abdomen. Abdominal computed tomography revealed an inhomogeneous soft tissue mass with target sign and intussusception of small intestine was suspected. Emergency laparotomy showed jejunojejunal intussusception involving ∼30 cm of jejunum with multiple tumors on the mesentery surface extending over the whole bowel mesenteric and peritoneal surfaces. One of the mesenteric tumors formed the leading point of the intussusception. Segmental resection of jejunum with primary anastomosis was done. Some larger tumors were resected but most of the other tumors were left in place because they were small and numerous and total resection was impossible. Pathology confirmed that the lesions were benign mesenteric calcifying fibrous pseudotumors. In such patients, surgery might be curative. If a large segment of the bowel is affected by calcifying fibrous pseudo-tumor, smaller pseudotumors might be left in place because these tend to be asymptomatic. But they might become the leading points of recurrent intussusception.

Key Words:  calcifying fibrous pseudotumor , intussusception

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References 

  1. Kutluk T , Emir S , Karnak I , et al.   Mesenteric inflammatory pseudotumor: unusual presentation with leukemoid reaction and massive calcified mass . J Pediatr Hematol Oncol . 2002;24:158–159
  2. Akman C , Dincbas FO , Oz B , et al.   Unusual cause of dysphagia: inflammatory pseudotumor of the lung . South Med J . 2005;98:665–668
  3. Van Dorpe J , Ectors N , Geboes K , et al.   Is calcifying fibrous pseudotumor a late sclerosing stage of inflammatory myofibroblastic tumor? . Am J Surg Pathol . 1999;23:329–335
  4. Kim TS , Han J , Kim GY , et al.   Pulmonary inflammatory pseudotumor CT features with pathologic correlation . J Comput Assist Tomogr . 2005;29:633–639
  5. Kocova L , Michal M , Sulc M , et al.   Calcifying fibrous pseudotumor of visceral peritoneum . Histopathology . 1997;31:182–184
  6. Khanafshar E , Phillipson J , Schammel DP , et al.   Inflammatory myofibroblastic tumor of the breast . Ann Diagn Pathol . 2005;9:123–129
  7. Fukunaga M , Kikuchi Y , Endo Y , et al.   Calcifying fibrous pseudotumor . Pathol Int. . 1997;47:60–63
  8. Sharon WW , John R . Goldblum . In: Soft Tissue Tumors . 4th edition. Philadelphia: Mosby; 2001;p. 396–399
  9. Takeuchi K , Tsuzuki Y , Ando T , et al.   The diagnosis and treatment of adult intussusception . J Clin Gastroenterol . 2003;36:18–21
  10. Tung SP , Chern CH , Chen JD , et al.   Epigastralgia with tarry stools in a middle-aged female caused by jejunal intussusception due to harmatoma . Emerg Radiol . 2005;11:298–300
  11. Azar T , Berger DL . Adult intussusception . Ann Surg . 1997;226:134–138
  12. Vijayaraghavan R , Sujatha Y , Santosh KV , et al.   Inflammatory fibroid polyp of jejunum causing jejuno-jejunal intussusception . Indian J Gastroenterol . 2004;23:190–192

PII: S0929-6646(09)60298-9

doi:10.1016/S0929-6646(09)60298-9

Journal of the Formosan Medical Association
Volume 106, Issue 6 , Pages 485-489, 2007